Sudden sensorineural hearing loss: Difference between revisions

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==Background==
===Epidemiology===
===Epidemiology===
*Mostly idiopathic
*Mostly idiopathic
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*Men and women affected equally
*Men and women affected equally


===Clinical Manifestations===
==Clinical Manifestations==
*Immediate/rapid hearing loss or hearing loss upon awakening
*Immediate/rapid hearing loss or hearing loss upon awakening
*Mostly unilateral hearing loss
*Mostly unilateral hearing loss
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*No sign of obstruction or OM on physical exam
*No sign of obstruction or OM on physical exam


===Diagnosis===
==Diagnosis==
*[[Eponyms_(T-Z)#Weber_test|Weber test]] and [[Eponyms_(Q-S)#Rinne_test|Rinne test]]
*[[Eponyms_(T-Z)#Weber_test|Weber test]] and [[Eponyms_(Q-S)#Rinne_test|Rinne test]]
*Otoscopic exam to r/o OM, OE, foreign bodies, perforated TM or cholesteatoma
*Otoscopic exam to r/o OM, OE, foreign bodies, perforated TM or cholesteatoma
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*MRI to r/o acoustic neuroma, perilymphatic fistula, Ménière’s disease, vascular insufficiency, MS
*MRI to r/o acoustic neuroma, perilymphatic fistula, Ménière’s disease, vascular insufficiency, MS


===Differential Diagnoses===
==Differential Diagnoses==
*Acute stroke, usually AICA occlusion
*Acute [[stroke]], usually AICA occlusion
*[[Multiple Sclerosis]]
*[[Multiple Sclerosis]]
*Meningitis
*[[Meningitis]]
*Vestibular schwannomas
*Vestibular schwannomas
*Migrainous infarction
*Migrainous infarction
*Acute otitis media
*[[Acute otitis media]]
*Traumatic TM rupture
*Traumatic TM rupture


===Treatment===
===Treatment===
*Glucocorticoids orally (prednisone 1 mg/kg/day up to 60 mg maximum for 10-14 days or dexamethasone 300 mg daily for 3 days)
*Glucocorticoids orally ([[prednisone]] 1 mg/kg/day up to 60 mg maximum for 10-14 days or [[dexamethasone]] 300 mg daily for 3 days)
*Glucocorticoids locally (intratympanic instillation, dexamethasone 10 to 24 mg/mL or methylprednisolone 30 to 40 mg/mL) if refractory to oral GCs
*Glucocorticoids locally (intratympanic instillation, [[dexamethasone]] 10 to 24 mg/mL or [[methylprednisolone]] 30 to 40 mg/mL) if refractory to oral GCs
*Antivirals for possible HSV-1 infection (valacyclovir 1g TID or famciclovir 500mg TID)
*Antivirals for possible [[HSV-1]] infection ([[valacyclovir]] 1g TID or [[famciclovir]] 500mg TID)


===Prognosis===
==Prognosis==
*Spontaneous improvement is common
*Spontaneous improvement is common
*Better prognosis if high- or low-frequency hearing loss pattern rather than flat across all frequencies
*Better prognosis if high- or low-frequency hearing loss pattern rather than flat across all frequencies
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*Worse in patients with vertigo
*Worse in patients with vertigo


===Follow-Up===
==Follow-Up==
*Audiogram in six months after initial diagnosis
*Audiogram in six months after initial diagnosis
*Possible auditory rehabilitation for patients with permanent hearing loss
*Possible auditory rehabilitation for patients with permanent hearing loss
*Consider assistive hearing devices
*Consider assistive hearing devices
==See Also==


==Sources==
==Sources==
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#Weber PC.  Etiology of hearing loss in adults.  In: UpToDate.  Accessed Sept 22 2014.
#Weber PC.  Etiology of hearing loss in adults.  In: UpToDate.  Accessed Sept 22 2014.
#Molina, FJ.  Hearing Loss, Chapter 18.  Tintinalli’s Emergency Medicine.
#Molina, FJ.  Hearing Loss, Chapter 18.  Tintinalli’s Emergency Medicine.
[[Category:ENT]]

Revision as of 01:45, 2 October 2014

Background

Epidemiology

  • Mostly idiopathic
  • Prognosis depends on severity of hearing loss
  • Incidence estimates range from 2-20 per 100,000 people per year
  • Most commonly 43-53 years of age
  • Men and women affected equally

Clinical Manifestations

  • Immediate/rapid hearing loss or hearing loss upon awakening
  • Mostly unilateral hearing loss
  • Sensation of blocked or full ear, patient doesn’t recognize hearing is gone
  • Difficulty in localizing sound
  • Tinnitus is common
  • Some patients report vertigo
  • Occasionally ear pain is present
  • No sign of obstruction or OM on physical exam

Diagnosis

  • Weber test and Rinne test
  • Otoscopic exam to r/o OM, OE, foreign bodies, perforated TM or cholesteatoma
  • Remove impacted cerumen and re-examine
  • Complete Neurologic Exam to r/o stroke
  • Audiometric evaluation
  • MRI to r/o acoustic neuroma, perilymphatic fistula, Ménière’s disease, vascular insufficiency, MS

Differential Diagnoses

Treatment

Prognosis

  • Spontaneous improvement is common
  • Better prognosis if high- or low-frequency hearing loss pattern rather than flat across all frequencies
  • Around 2/3 of patients with SSHL will regain hearing in the affected ear
  • Worse prognosis in older patients
  • Worse in patients with vertigo

Follow-Up

  • Audiogram in six months after initial diagnosis
  • Possible auditory rehabilitation for patients with permanent hearing loss
  • Consider assistive hearing devices

See Also

Sources

  1. Weber PC. Sudden sensorineural hearing loss. In: UpToDate. Accessed Sept 22 2014.
  2. Weber PC. Etiology of hearing loss in adults. In: UpToDate. Accessed Sept 22 2014.
  3. Molina, FJ. Hearing Loss, Chapter 18. Tintinalli’s Emergency Medicine.