Budd-Chiari syndrome: Difference between revisions

Latest revision as of 12:25, 7 January 2026

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Background

Posterior abdominal wall, after removal of the peritoneum, showing kidneys, suprarenal capsules, and great vessels. (Hepatic veins labeled at center top.)

Rare
Caused by occlusion of hepatic veins, 75% primary (thrombosis), 25% secondary (compression by mass)
Fulminant, acute, chronic, or asymptomatic.

Clinical Features

Classic triad:

Differential Diagnosis

RUQ Pain

Gallbladder disease
- Symptomatic cholelithiasis (biliary colic)
- Choledocholithiasis
- Acute cholecystitis
- Ascending cholangitis
- Acalculous cholecystitis
Pancreatitis
Acute hepatitis
Pancreatitis
GERD
Appendicitis (retrocecal)
Pyogenic liver abscess
Bowel obstruction
Cirrhosis
Budd-Chiari syndrome
GU
Other
- Hepatomegaly due to CHF
- Peptic ulcer disease with or without perforation
- Pneumonia
- Herpes zoster
- Myocardial ischemia
- Pulmonary embolism
- Abdominal aortic aneurysm

Evaluation

Budd–Chiari syndrome secondary to cancer, note clot in the inferior vena cava and the metastasis in the liver.

LFTs, BMP, LDH
Ultrasound, retrograde angiography
CT and MRI less sensitive

Management

Sodium restriction, diuretics, anticoagulants
Venous shunts or TIPS
Liver transplant

Disposition

External Links

References

Authors:

@@ Line 1: / Line 1: @@
-==Background==
+<languages/>
+<translate>
+==Background== <!--T:1-->
+<!--T:2-->
+[[File:Gray1121.png|thumb|Posterior abdominal wall, after removal of the peritoneum, showing kidneys, suprarenal capsules, and great vessels. (Hepatic veins labeled at center top.)]]
 *Rare
 *Caused by occlusion of hepatic veins, 75% primary (thrombosis), 25% secondary (compression by mass)
 *Fulminant, acute, chronic, or asymptomatic.
-==Clinical Features==
-*Classic triad: [[abdominal pain]], [[ascites]], and [[hepatomegaly]]
-==Differential Diagnosis==
-*[[Hepatitis]]
+==Clinical Features== <!--T:3-->
-*[[Cirrhosis]]
-==Evaluation==
+<!--T:4-->
-*[[LFTs]], BMP, LDH
+Classic triad:
-*[[RUQ ultrasound|Ultrasound]], retrograde angiography
+#[[Special:MyLanguage/Abdominal pain|Abdominal pain]]
+#[[Special:MyLanguage/Ascites|Ascites]]
+#[[Special:MyLanguage/Hepatomegaly|Hepatomegaly]]
+==Differential Diagnosis== <!--T:5-->
+</translate>
+{{DDX RUQ}}
+<translate>
+==Evaluation== <!--T:6-->
+<!--T:7-->
+[[File:Buddchiari2.png|thumb|Budd–Chiari syndrome secondary to cancer, note clot in the inferior vena cava and the metastasis in the liver.]]
+*[[Special:MyLanguage/LFTs|LFTs]], BMP, LDH
+*[[Special:MyLanguage/RUQ ultrasound|Ultrasound]], retrograde angiography
 *CT and MRI less sensitive
-==Management==
-*Sodium restriction, [[diuretics]], [[anticoagulants]]
-*Venous shunts or [[TIPS]]
+==Management== <!--T:8-->
+<!--T:9-->
+*Sodium restriction, [[Special:MyLanguage/diuretics|diuretics]], [[Special:MyLanguage/anticoagulants|anticoagulants]]
+*Venous shunts or [[Special:MyLanguage/TIPS|TIPS]]
 *Liver transplant
-==Disposition==
-==See Also==
-[[Portal vein thrombosis]] (PVT)
-==External Links==
+==Disposition== <!--T:10-->
-==References==
+==See Also== <!--T:11-->
+<!--T:12-->
+*[[Special:MyLanguage/Portal vein thrombosis|Portal vein thrombosis]]
+==External Links== <!--T:13-->
+==References== <!--T:14-->
+<!--T:15-->
 <references/>
+<!--T:16-->
 [[Category:GI]]
+</translate>