Difference between revisions of "Restrictive cardiomyopathy"
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Revision as of 04:47, 13 July 2016
Contents
Background
- Muscle is stiff from fibrosis or infiltrating process
- EF is usually normal
- Form of diastolic dysfunction (difficulty filling)
- Must distinguish from constrictive pericarditis
Differential Diagnosis
Cardiomyopathy
- Dilated cardiomyopathy
- Hypertrophic cardiomyopathy
- Restrictive cardiomyopathy
- Peripartum cardiomyopathy
- Takotsubo cardiomyopathy
- Arrhythmogenic right ventricular dysplasia
- Restrictive cardiomyopathy ddx
- Idiopathic
- Familial noninfiltrative disease
- Infiltrative disease (amyloidosis, sarcoidosis, Gaucher, Hurler)
- Storage diseases (hemachromatosis, Fabry, glycogen/lysosomal storage diseases)
- Diabetes
- Scleroderma
- Endomyocardial fibrosis (hypereosinophilic syndrome, medication toxicity)
- Radiation, chemotherapy (doxorubicin)
- Metastatic disease, carcinoid syndrome
Diagnosis
- Consider if CHF but no evidence of cardiomegaly or systolic dysfunction
Management
- Symptom directed (diuretics and ACEI)