Difference between revisions of "Restrictive cardiomyopathy"
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==Differential Diagnosis== | ==Differential Diagnosis== | ||
{{Cardiomyopathy DDX}} | {{Cardiomyopathy DDX}} | ||
+ | *Restrictive cardiomyopathy ddx | ||
+ | **Idiopathic | ||
+ | **Familial noninfiltrative disease | ||
+ | **Infiltrative disease (amyloidosis, sarcoidosis, Gaucher, Hurler) | ||
+ | **Storage diseases (hemachromatosis, Fabry, glycogen/lysosomal storage diseases) | ||
+ | **Diabetes | ||
+ | **Scleroderma | ||
+ | **Endomyocardial fibrosis (hypereosinophilic syndrome, medication toxicity) | ||
+ | **Radiation, chemotherapy | ||
+ | **Metastatic disease, carcinoid syndrome | ||
==Diagnosis== | ==Diagnosis== |
Revision as of 00:50, 5 January 2016
Contents
Background
- Must distinguish from constrictive pericarditis
Differential Diagnosis
Cardiomyopathy
- Dilated cardiomyopathy
- Hypertrophic cardiomyopathy
- Restrictive cardiomyopathy
- Peripartum cardiomyopathy
- Takotsubo cardiomyopathy
- Arrhythmogenic right ventricular dysplasia
- Restrictive cardiomyopathy ddx
- Idiopathic
- Familial noninfiltrative disease
- Infiltrative disease (amyloidosis, sarcoidosis, Gaucher, Hurler)
- Storage diseases (hemachromatosis, Fabry, glycogen/lysosomal storage diseases)
- Diabetes
- Scleroderma
- Endomyocardial fibrosis (hypereosinophilic syndrome, medication toxicity)
- Radiation, chemotherapy
- Metastatic disease, carcinoid syndrome
Diagnosis
- Consider if CHF but no e/o cardiomegaly or systolic dysfunction
Treatment
- Symptom directed (diuretics and ACEI)
See Also
Source
Tintinalli