Budd-Chiari syndrome
Background
- Rare; caused by occlusion of hepatic veins, 75% primary (thrombosis), 25% secondary (compression by mass)
- Fulminant, acute, chronic, or asymptomatic.
Clinical Features
- Classic triad: abdominal pain, ascites, and hepatomegaly
Differential Diagnosis
Evaluation
- LFTs, creatinine, urea, electrolytes, LDH
- Ultrasound, retrograde angiography
- CT and MRI less sensitive
Management
- sodium restriction, diuretics, anticoagulants
- venous shunts or TIPS
- liver transplant