Budd-Chiari syndrome: Difference between revisions

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==Background==
==Background==
*Rare; caused by occlusion of hepatic veins, 75% primary (thrombosis), 25% secondary (compression by mass)
*Rare
*Caused by occlusion of hepatic veins, 75% primary (thrombosis), 25% secondary (compression by mass)
*Fulminant, acute, chronic, or asymptomatic.
*Fulminant, acute, chronic, or asymptomatic.
==Clinical Features==
==Clinical Features==
* Classic triad: abdominal pain, [[ascites]], and [[hepatomegaly]]  
* Classic triad: [[abdominal pain]], [[ascites]], and [[hepatomegaly]]  
==Differential Diagnosis==
==Differential Diagnosis==
*[[Hepatitis]]
*[[Hepatitis]]
*[[Cirrhosis]]
*[[Cirrhosis]]
==Evaluation==
==Evaluation==
*LFTs, creatinine, urea, electrolytes, LDH
*[[LFTs]], BMP, LDH
* Ultrasound, retrograde angiography
* Ultrasound, retrograde angiography
*CT and MRI less sensitive
*CT and MRI less sensitive
==Management==
==Management==
*sodium restriction, diuretics, anticoagulants
*Sodium restriction, [[diuretics]], [[anticoagulants]]
*venous shunts or TIPS
*venous shunts or TIPS
*liver transplant
*liver transplant
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<references/>
<references/>


[[Category:Neurology]]
[[Category:GI]]

Revision as of 17:48, 27 March 2017

Background

  • Rare
  • Caused by occlusion of hepatic veins, 75% primary (thrombosis), 25% secondary (compression by mass)
  • Fulminant, acute, chronic, or asymptomatic.

Clinical Features

Differential Diagnosis

Evaluation

  • LFTs, BMP, LDH
  • Ultrasound, retrograde angiography
  • CT and MRI less sensitive

Management

Disposition

See Also

External Links

References